(D82.8) Immunodeficiency associated with other specified major defects

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57 978 in individuals diagnosis immunodeficiency associated with other specified major defects confirmed
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2 889 deaths with diagnosis immunodeficiency associated with other specified major defects
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5% mortality rate associated with the disease immunodeficiency associated with other specified major defects

Diagnosis immunodeficiency associated with other specified major defects is diagnosed Men are 15.88% more likely than Women

33 592

Men receive the diagnosis immunodeficiency associated with other specified major defects

1 730 (5.2 %)

Died from this diagnosis.

100
95
90
85
80
75
70
65
60
55
50
45
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35
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15
10
5
0
24 386

Women receive the diagnosis immunodeficiency associated with other specified major defects

1 159 (4.8 %)

Died from this diagnosis.

Risk Group for the Disease immunodeficiency associated with other specified major defects - Men and Women aged 5-9

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In Men diagnosis is most often set at age 0-19, 25-29, 40-44, 50-64, 70-84
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Less common in men the disease occurs at Age 20-24, 30-39, 45-49, 65-69, 85-95+Less common in women the disease occurs at Age 40-44, 50-69, 80-95+
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In Women diagnosis is most often set at age 0-39, 45-49, 70-79

Disease Features immunodeficiency associated with other specified major defects

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Absence or low individual and public risk
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Immunodeficiency associated with other specified major defects - what does this mean

Immunodeficiency associated with other specified major defects is a condition in which the immune system is weakened due to a defect in a major organ system, such as the heart, lungs, kidneys, or liver. this can lead to an increased risk of infection, as the body is unable to fight off foreign organisms.

What happens during the disease - immunodeficiency associated with other specified major defects

Immunodeficiency associated with other specified major defects is caused by a combination of genetic and environmental factors. these include mutations in genes that are important for the development and functioning of the immune system, such as t-cell receptor genes, as well as environmental exposures that can damage the immune system, such as toxins, radiation, and certain medications. these factors can lead to a decreased ability of the immune system to respond to infections, leading to increased susceptibility to infection and other complications.

Clinical Pattern

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How does a doctor diagnose

  • Complete physical examination
  • Blood tests to measure levels of antibodies and other immune system components
  • Imaging tests such as X-rays, CT scans, and MRI scans
  • Tissue biopsy
  • Genetic testing
Additions:
  • Pulmonary Function Test
  • Allergy Testing

Treatment and Medical Assistance

Main Goal: To treat Immunodeficiency associated with other specified major defects.
  • Provide immune boosting medications such as intravenous immunoglobulin (IVIG) or other immune-modulating therapies.
  • Administer antibiotics to prevent or treat infections.
  • Provide nutritional support to optimize growth and development.
  • Manage any associated conditions, such as allergies, asthma, or auto-immune diseases.
  • Monitor for any signs of infection and treat promptly.
  • Provide education to the patient and their family about the disease and how to manage it.
  • Refer to a specialist if needed.
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8 Days of Hospitalization Required
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55 Hours Required for Outpatient Treatment

Immunodeficiency associated with other specified major defects - Prevention

The best way to prevent immunodeficiency associated with other specified major defects is to ensure that individuals have access to adequate health care and nutrition, and that they receive regular vaccinations to protect them from infectious diseases. additionally, individuals should be encouraged to practice good hygiene and to seek medical attention if they experience any symptoms of an underlying condition.