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(D83.1) Common variable immunodeficiency with predominant immunoregulatory t-cell disorders
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174 785 in individuals diagnosis common variable immunodeficiency with predominant immunoregulatory t-cell disorders confirmed
3 186 deaths with diagnosis common variable immunodeficiency with predominant immunoregulatory t-cell disorders
2% mortality rate associated with the disease common variable immunodeficiency with predominant immunoregulatory t-cell disorders
Diagnosis common variable immunodeficiency with predominant immunoregulatory t-cell disorders is diagnosed Men are 19.46% more likely than Women
104 402
Men receive the diagnosis common variable immunodeficiency with predominant immunoregulatory t-cell disorders
1 828 (1.8 %)Died from this diagnosis.
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70 383
Women receive the diagnosis common variable immunodeficiency with predominant immunoregulatory t-cell disorders
1 358 (1.9 %)Died from this diagnosis.
Risk Group for the Disease common variable immunodeficiency with predominant immunoregulatory t-cell disorders - Men and Women aged 0-5
In Men diagnosis is most often set at age 0-64, 70-89
Less common in men the disease occurs at Age 65-69, 90-95+Less common in women the disease occurs at Age 80-89, 95+
In Women diagnosis is most often set at age 0-79, 90-94
Disease Features common variable immunodeficiency with predominant immunoregulatory t-cell disorders
Absence or low individual and public risk
Common variable immunodeficiency with predominant immunoregulatory t-cell disorders - what does this mean
Common variable immunodeficiency with predominant immunoregulatory t-cell disorders occurs when the body doesn't produce enough t-cells, which are a type of white blood cell responsible for regulating the immune system. this can lead to recurrent infections, autoimmune disorders, and other complications.
What happens during the disease - common variable immunodeficiency with predominant immunoregulatory t-cell disorders
Common variable immunodeficiency with predominant immunoregulatory t-cell disorders is a rare and complex disorder characterized by a decrease in the number of circulating b and t cells, resulting in an impaired ability to produce antibodies and fight infections. the underlying cause of the disorder is a mutation in the gene responsible for the production of certain proteins that regulate the activity of t cells. this leads to an abnormal production of cytokines by t cells, resulting in an impaired ability to respond to antigens and produce antibodies. the decreased number of b and t cells also leads to an increased susceptibility to infections.
Clinical Pattern
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How does a doctor diagnose
- Complete blood count (CBC)
- Flow cytometry analysis
- T-cell receptor excision circles (TRECs) assay
- Immunoglobulin levels
- T-cell subset analysis
- Lymphocyte proliferation assay
- CT/MRI scan of the chest, abdomen, and pelvis
Treatment and Medical Assistance
Main Goal: To improve the patient's immune system.
- Administering immunoglobulin replacement therapy
- Prescribing immune-modulating medications
- Providing vaccinations
- Prescribing antibiotics to prevent and treat infections
- Monitoring for signs and symptoms of infection
- Educating the patient on proper hygiene and nutrition
- Referring the patient to a specialist for further assessment and treatment
10 Days of Hospitalization Required
126 Hours Required for Outpatient Treatment
Common variable immunodeficiency with predominant immunoregulatory t-cell disorders - Prevention
Common variable immunodeficiency with predominant immunoregulatory t-cell disorders can be prevented by immunization, good hygiene practices, proper nutrition, and regular medical check-ups. vaccines are especially important to help protect against infection and reduce the risk of developing this disorder. additionally, avoiding contact with people who are ill, avoiding smoking, and reducing stress are important preventive measures.