(E84.0) Cystic fibrosis with pulmonary manifestations

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580 693 in individuals diagnosis cystic fibrosis with pulmonary manifestations confirmed
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10 360 deaths with diagnosis cystic fibrosis with pulmonary manifestations
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2% mortality rate associated with the disease cystic fibrosis with pulmonary manifestations

Diagnosis cystic fibrosis with pulmonary manifestations is diagnosed Women are 3.58% more likely than Men

279 960

Men receive the diagnosis cystic fibrosis with pulmonary manifestations

4 512 (1.6 %)

Died from this diagnosis.

100
95
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85
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75
70
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55
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5
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300 733

Women receive the diagnosis cystic fibrosis with pulmonary manifestations

5 848 (1.9 %)

Died from this diagnosis.

Risk Group for the Disease cystic fibrosis with pulmonary manifestations - Men aged 15-19 and Women aged 10-14

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In Men diagnosis is most often set at age 0-79
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Less common in men the disease occurs at Age 80-95+Less common in women the disease occurs at Age 85-95+
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In Women diagnosis is most often set at age 0-84

Disease Features cystic fibrosis with pulmonary manifestations

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Absence or low individual and public risk
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Cystic fibrosis with pulmonary manifestations - what does this mean

Cystic fibrosis with pulmonary manifestations is a genetic disorder caused by a mutation in the cftr gene, which causes excessive mucus production in the lungs that leads to recurrent infections, inflammation, and scarring. this can cause difficulty breathing and other respiratory symptoms, such as a persistent cough, wheezing, and shortness of breath.

What happens during the disease - cystic fibrosis with pulmonary manifestations

Cystic fibrosis is a genetic disorder caused by a mutation in the cystic fibrosis transmembrane conductance regulator (cftr) gene. this mutation results in a defective protein that affects the body's ability to regulate the movement of chloride ions in and out of cells. this leads to an accumulation of thick, sticky mucus in the lungs, pancreas, and other organs, which can cause chronic inflammation and infection, as well as blockages of the airways, leading to respiratory symptoms such as coughing, wheezing, and shortness of breath.

Clinical Pattern

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How does a doctor diagnose

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Treatment and Medical Assistance

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21 Days of Hospitalization Required
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Average Time for Outpatient Care Not Established

Cystic fibrosis with pulmonary manifestations - Prevention

Cystic fibrosis with pulmonary manifestations can be prevented by following a healthy lifestyle, avoiding smoking, and getting regular vaccinations. additionally, genetic counseling is recommended for those with a family history of the disease.