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(D76.1) Haemophagocytic lymphohistiocytosis
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80 032 in individuals diagnosis haemophagocytic lymphohistiocytosis confirmed
7 898 deaths with diagnosis haemophagocytic lymphohistiocytosis
10% mortality rate associated with the disease haemophagocytic lymphohistiocytosis
Diagnosis haemophagocytic lymphohistiocytosis is diagnosed Men are 32.15% more likely than Women
52 883
Men receive the diagnosis haemophagocytic lymphohistiocytosis
4 637 (8.8 %)Died from this diagnosis.
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27 149
Women receive the diagnosis haemophagocytic lymphohistiocytosis
3 261 (12.0 %)Died from this diagnosis.
Risk Group for the Disease haemophagocytic lymphohistiocytosis - Men and Women aged 0-5
In Men diagnosis is most often set at age 0-94
Less common in men the disease occurs at Age 95+Less common in women the disease occurs at Age 75-79, 85-95+
In Women diagnosis is most often set at age 0-74, 80-84
Disease Features haemophagocytic lymphohistiocytosis
Absence or low individual and public risk
Haemophagocytic lymphohistiocytosis - what does this mean
Haemophagocytic lymphohistiocytosis (hlh) is a rare and potentially life-threatening disorder in which the body’s immune system becomes overactive and begins to attack its own cells and organs. this overactivity causes the body to produce too many lymphocytes and histiocytes, which can then attack and damage organs, leading to organ failure. hlh is caused by a variety of genetic and acquired conditions, including infections, malignancies, and autoimmune disorders.
What happens during the disease - haemophagocytic lymphohistiocytosis
Haemophagocytic lymphohistiocytosis is a rare disorder caused by an overactive immune system. it is caused by a dysfunction of the immune system, which results in the overproduction and activation of certain immune cells, such as histiocytes and lymphocytes. these cells then enter the bloodstream and cause an excessive inflammatory response, leading to the destruction of healthy cells and tissues, as well as the release of inflammatory cytokines. this can lead to organ damage, anemia, and a range of other symptoms.
Clinical Pattern
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How does a doctor diagnose
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Treatment and Medical Assistance
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14 Days of Hospitalization Required
Average Time for Outpatient Care Not Established
Haemophagocytic lymphohistiocytosis - Prevention
Haemophagocytic lymphohistiocytosis is best prevented through early diagnosis and prompt treatment of primary infections and immune disorders, as well as vaccinations for preventable diseases. it is important to maintain a healthy lifestyle, including regular exercise, a balanced diet, and avoiding smoking and alcohol. additionally, regular check-ups with a healthcare provider can help to identify any potential issues early on and allow for prompt treatment.