(L44.0) Pityriasis rubra pilaris

More details coming soon

Icon
36 954 in individuals diagnosis pityriasis rubra pilaris confirmed

Diagnosis pityriasis rubra pilaris is diagnosed Men are 1.39% more likely than Women

18 733

Men receive the diagnosis pityriasis rubra pilaris

0 (less than 0.1%)

Died from this diagnosis.

100
95
90
85
80
75
70
65
60
55
50
45
40
35
30
25
20
15
10
5
0
18 221

Women receive the diagnosis pityriasis rubra pilaris

0 (less than 0.1%)

Died from this diagnosis.

Risk Group for the Disease pityriasis rubra pilaris - Men aged 55-59 and Women aged 60-64

Icon
In Men diagnosis is most often set at age 0-89
Icon
Less common in men the disease occurs at Age 90-95+Less common in women the disease occurs at Age 0-1, 80-84, 90-95+
Icon
In Women diagnosis is most often set at age 0-79, 85-89

Disease Features pityriasis rubra pilaris

Icon
Absence or low individual and public risk
Icon

Pityriasis rubra pilaris - what does this mean

Pityriasis rubra pilaris is an uncommon skin disorder that is characterized by red, scaly patches on the skin that are often accompanied by thickening of the skin on the palms and soles. it is a chronic condition that can last for months or even years and is caused by an abnormal response of the immune system.

What happens during the disease - pityriasis rubra pilaris

Pityriasis rubra pilaris (prp) is an inflammatory skin disorder caused by an abnormal immune response. it is believed to be triggered by a combination of genetic and environmental factors, such as uv exposure, infections, and certain medications. the abnormal immune response leads to an increase in pro-inflammatory cytokines, which in turn leads to inflammation and thickening of the skin. this results in red, scaly patches on the skin, as well as other symptoms such as pustules, follicular hyperkeratosis, and hyperpigmentation.

Clinical Pattern

More details coming soon

How does a doctor diagnose

  • Physical examination of the skin
  • Laboratory tests, such as a complete blood count, blood chemistry, and urinalysis
  • Skin biopsy to confirm the diagnosis
  • Imaging tests, such as X-rays or ultrasound
  • Tests to rule out other skin conditions, such as psoriasis
  • Genetic testing to check for inherited forms of the condition

Treatment and Medical Assistance

Main goal of the treatment: To reduce inflammation and control scaling.
  • Prescribe topical corticosteroids or topical calcineurin inhibitors.
  • Prescribe oral retinoids (eg, acitretin).
  • Prescribe hydroxychloroquine for severe cases.
  • Prescribe ultraviolet light therapy.
  • Prescribe systemic antibiotics.
  • Prescribe topical antifungals.
  • Prescribe topical immunomodulators.
  • Prescribe oral immunosuppressants.
  • Prescribe topical retinoids.
  • Prescribe topical vitamin D analogs.
  • Prescribe oral biologics.
Icon
17 Days of Hospitalization Required
Icon
Average Time for Outpatient Care Not Established

Pityriasis rubra pilaris - Prevention

Pityriasis rubra pilaris can be prevented by avoiding excessive sun exposure, using sunscreen, and avoiding any skin injuries that can be caused by scratching or other irritations. additionally, individuals should practice good hygiene and keep skin clean and moisturized.