(L94.3) Sclerodactyly

More details coming soon

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285 592 in individuals diagnosis sclerodactyly confirmed
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1 434 deaths with diagnosis sclerodactyly
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1% mortality rate associated with the disease sclerodactyly

Diagnosis sclerodactyly is diagnosed Women are 50.49% more likely than Men

70 701

Men receive the diagnosis sclerodactyly

1 434 (2.0 %)

Died from this diagnosis.

100
95
90
85
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75
70
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50
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214 891

Women receive the diagnosis sclerodactyly

0 (less than 0.1%)

Died from this diagnosis.

Risk Group for the Disease sclerodactyly - Men and Women aged 10-14

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In Men diagnosis is most often set at age 0-89
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Less common in men the disease occurs at Age 90-95+Less common in women the disease occurs at Age 95+
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In Women diagnosis is most often set at age 0-94

Disease Features sclerodactyly

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Absence or low individual and public risk
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Sclerodactyly - what does this mean

Sclerodactyly is a skin condition caused by the hardening and tightening of the skin on the fingers and hands. it is caused by the accumulation of collagen fibers and other proteins in the skin, leading to thickening and tightening of the skin on the fingers and hands. it is often associated with other conditions such as systemic sclerosis, raynaud's phenomenon, and sjogren's syndrome.

What happens during the disease - sclerodactyly

Sclerodactyly is a connective tissue disorder caused by an abnormal accumulation of collagen fibers in the skin, leading to thickening and tightening of the skin on the fingers and toes. this can lead to a decrease in blood flow, resulting in decreased mobility and a decrease in sensation in the affected areas. in some cases, this can cause joint contractures and deformities, leading to a decrease in function.

Clinical Pattern

More details coming soon

How does a doctor diagnose

  • Obtaining a detailed medical history and physical examination of the patient
  • Skin biopsy to confirm the diagnosis
  • Laboratory tests to evaluate for possible underlying causes
  • Imaging studies such as X-ray, MRI, and ultrasound
  • Blood tests to assess for inflammation, organ damage, and other abnormalities
  • Genetic testing to identify any mutations in the genes associated with sclerodactyly
Additions:
  • Consultation with a rheumatologist to rule out other causes of the symptoms
  • Assessment of hand function to determine any functional limitations

Treatment and Medical Assistance

Main goal of the treatment: Reduce symptoms of Sclerodactyly
  • Medications to reduce inflammation
  • Physical therapy to increase joint mobility
  • Exercises to strengthen muscles
  • Occupational therapy to improve hand function
  • Splinting to protect joints
  • Topical creams to reduce itching and discomfort
  • Laser therapy to reduce pain
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13 Days of Hospitalization Required
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Average Time for Outpatient Care Not Established

Sclerodactyly - Prevention

The best way to prevent sclerodactyly is to practice good skin hygiene, wear protective clothing, and avoid direct exposure to the sun. additionally, it is important to keep the skin moisturized and to avoid any activities that may cause trauma to the skin, such as scratching or rubbing. finally, it is important to seek medical attention if any signs of sclerodactyly develop.