(Q22.0) Pulmonary valve atresia

More details coming soon

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258 814 in individuals diagnosis pulmonary valve atresia confirmed
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5 601 deaths with diagnosis pulmonary valve atresia
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2% mortality rate associated with the disease pulmonary valve atresia

Diagnosis pulmonary valve atresia is diagnosed Men are 2.44% more likely than Women

132 569

Men receive the diagnosis pulmonary valve atresia

3 043 (2.3 %)

Died from this diagnosis.

100
95
90
85
80
75
70
65
60
55
50
45
40
35
30
25
20
15
10
5
0
126 245

Women receive the diagnosis pulmonary valve atresia

2 558 (2.0 %)

Died from this diagnosis.

Risk Group for the Disease pulmonary valve atresia - Men and Women aged 0

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In Men diagnosis is most often set at age 0-79
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Less common in men the disease occurs at Age 80-95+Less common in women the disease occurs at Age 80-95+
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In Women diagnosis is most often set at age 0-79

Disease Features pulmonary valve atresia

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Absence or low individual and public risk
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Pulmonary valve atresia - what does this mean

Pulmonary valve atresia is a congenital heart defect in which the pulmonary valve fails to form, resulting in a complete blockage of blood flow from the right ventricle to the pulmonary arteries. this defect prevents oxygen-poor blood from leaving the right ventricle and entering the pulmonary arteries to be delivered to the lungs.

What happens during the disease - pulmonary valve atresia

Pulmonary valve atresia is a congenital heart defect caused by abnormal development of the pulmonary valve during fetal development. this results in the valve being unable to open and close properly, leading to a lack of blood flow from the right ventricle to the pulmonary artery. this lack of blood flow can cause the right ventricle to become enlarged and weaker over time, leading to a decrease in oxygenated blood supply to the rest of the body. as a result, symptoms of this condition can include fatigue, shortness of breath, and difficulty breathing.

Clinical Pattern

More details coming soon

How does a doctor diagnose

  • Echocardiogram
  • Chest X-ray
  • Cardiac MRI
  • Cardiac Catheterization
  • Electrocardiogram (ECG)
  • Blood Tests

Treatment and Medical Assistance

Main goal of the treatment: To reduce the risk of complications associated with Pulmonary Valve Atresia.
  • Medication to reduce pulmonary hypertension
  • Surgery to create a connection between the right ventricle and the pulmonary artery
  • Surgery to insert a prosthetic valve
  • Regular monitoring of the patient's condition
  • Nutritional management
  • Regular exercise
  • Implantation of a pacemaker to regulate the heartbeat
  • Pulmonary valve balloon dilation
  • Antibiotic therapy to prevent infection
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15 Days of Hospitalization Required
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Average Time for Outpatient Care Not Established

Pulmonary valve atresia - Prevention

The best way to prevent pulmonary valve atresia is to maintain a healthy lifestyle, including regular exercise, eating a balanced diet, avoiding smoking and alcohol, and getting regular check-ups with a doctor. additionally, it is important to be aware of any family history of heart defects, and to seek medical attention if any symptoms of pulmonary valve atresia are present.