(Q26.5) Anomalous portal venous connection

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48 491 in individuals diagnosis anomalous portal venous connection confirmed
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3 041 deaths with diagnosis anomalous portal venous connection
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6% mortality rate associated with the disease anomalous portal venous connection

Diagnosis anomalous portal venous connection is diagnosed Men are 14.31% more likely than Women

27 715

Men receive the diagnosis anomalous portal venous connection

1 831 (6.6 %)

Died from this diagnosis.

100
95
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75
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55
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15
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20 776

Women receive the diagnosis anomalous portal venous connection

1 210 (5.8 %)

Died from this diagnosis.

Risk Group for the Disease anomalous portal venous connection - Men and Women aged 0

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In Men diagnosis is most often set at age 0-29, 35-64, 75-79
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Less common in men the disease occurs at Age 30-34, 65-74, 80-95+Less common in women the disease occurs at Age 70-79, 85-95+
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In Women diagnosis is most often set at age 0-69, 80-84

Disease Features anomalous portal venous connection

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Absence or low individual and public risk
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Anomalous portal venous connection - what does this mean

Anomalous portal venous connection is a congenital condition that occurs when the portal vein, which is responsible for carrying blood from the gastrointestinal tract to the liver, is connected abnormally to other veins in the abdomen, such as the splenic vein, the superior mesenteric vein, or the inferior vena cava. this can cause a variety of symptoms, such as abnormal liver function, an enlarged spleen, and portal hypertension.

What happens during the disease - anomalous portal venous connection

Anomalous portal venous connection is a congenital condition in which there is an abnormal connection between the portal vein and another vein, usually the inferior vena cava, leading to an increase in portal venous pressure. this increased pressure can lead to portal hypertension, which can cause liver damage, varices, and other complications. in some cases, the increased pressure can also cause a shunt between the portal vein and the systemic circulation, leading to systemic venous congestion, which can cause systemic symptoms such as fatigue, edema, and ascites.

Clinical Pattern

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How does a doctor diagnose

  • Physical examination
  • Ultrasound imaging
  • CT scan
  • MRI scan
  • Angiography
  • Endoscopic retrograde cholangiopancreatography (ERCP)
  • Liver biopsy

Treatment and Medical Assistance

Main goal: To treat Anomalous portal venous connection
  • Regular monitoring of the patient's condition
  • Prescribing medications to reduce the symptoms
  • Performing imaging tests to determine the extent of the disease
  • Surgical intervention to close the abnormally connected vessels
  • Instructing the patient on lifestyle modifications to reduce the risk of complications
  • Administering blood transfusions as needed
  • Providing emotional support to the patient and their family
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21 Days of Hospitalization Required
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Average Time for Outpatient Care Not Established

Anomalous portal venous connection - Prevention

The primary prevention of anomalous portal venous connection is to ensure that prenatal ultrasound screening is done to detect any potential abnormalities in the fetus. if detected early, the condition can be managed with appropriate medical care. additionally, if the condition is diagnosed in a newborn, it is important to consult a specialist for further evaluation and management.