(Q79.4) Prune belly syndrome

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203 021 in individuals diagnosis prune belly syndrome confirmed
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13 891 deaths with diagnosis prune belly syndrome
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7% mortality rate associated with the disease prune belly syndrome

Diagnosis prune belly syndrome is diagnosed Men are 2.86% more likely than Women

104 416

Men receive the diagnosis prune belly syndrome

7 358 (7.0 %)

Died from this diagnosis.

100
95
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98 605

Women receive the diagnosis prune belly syndrome

6 533 (6.6 %)

Died from this diagnosis.

Risk Group for the Disease prune belly syndrome - Men and Women aged 0

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In Men diagnosis is most often set at age 0-89
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Less common in men the disease occurs at Age 90-95+Less common in women the disease occurs at Age 95+
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In Women diagnosis is most often set at age 0-94

Disease Features prune belly syndrome

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Absence or low individual and public risk
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Prune belly syndrome - what does this mean

Prune belly syndrome is a rare genetic disorder caused by the absence or underdevelopment of the abdominal muscles, leading to the presence of lax abdominal skin, undescended testes, and urinary tract abnormalities. it is typically diagnosed shortly after birth.

What happens during the disease - prune belly syndrome

Prune belly syndrome is a rare genetic disorder that affects the development of the abdominal wall muscles, urinary system, and external genitalia. it is caused by a genetic mutation that affects the development of the abdominal wall muscles, urinary tract, and external genitalia. this mutation causes the abdominal wall muscles to be underdeveloped, resulting in a wrinkled or “prune belly” appearance. it also affects the development of the urinary tract, leading to obstruction of the ureters and bladder, and can cause kidney failure. in some cases, the external genitalia may be underdeveloped, leading to infertility.

Clinical Pattern

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How does a doctor diagnose

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Treatment and Medical Assistance

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25 Days of Hospitalization Required
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Average Time for Outpatient Care Not Established

Prune belly syndrome - Prevention

Prune belly syndrome can be prevented by avoiding risk factors such as smoking and alcohol consumption during pregnancy, and seeking regular prenatal care to ensure that any potential complications are identified and managed promptly. additionally, genetic counseling is recommended for couples with a family history of the condition.