(Q23.4) Hypoplastic left heart syndrome

More details coming soon

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454 048 in individuals diagnosis hypoplastic left heart syndrome confirmed
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13 887 deaths with diagnosis hypoplastic left heart syndrome
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3% mortality rate associated with the disease hypoplastic left heart syndrome

Diagnosis hypoplastic left heart syndrome is diagnosed Men are 34.83% more likely than Women

306 107

Men receive the diagnosis hypoplastic left heart syndrome

8 957 (2.9 %)

Died from this diagnosis.

100
95
90
85
80
75
70
65
60
55
50
45
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35
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15
10
5
0
147 941

Women receive the diagnosis hypoplastic left heart syndrome

4 930 (3.3 %)

Died from this diagnosis.

Risk Group for the Disease hypoplastic left heart syndrome - Men and Women aged 0

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In Men diagnosis is most often set at age 0-89
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Less common in men the disease occurs at Age 90-95+Less common in women the disease occurs at Age 95+
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In Women diagnosis is most often set at age 0-94

Disease Features hypoplastic left heart syndrome

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Absence or low individual and public risk
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Hypoplastic left heart syndrome - what does this mean

Hypoplastic left heart syndrome (hlhs) is a congenital heart defect in which the left side of the heart is severely underdeveloped. this results in the left ventricle, aorta, and mitral valve being too small to effectively pump oxygenated blood from the lungs to the body, leading to severe oxygen deprivation.

What happens during the disease - hypoplastic left heart syndrome

Hypoplastic left heart syndrome (hlhs) is a congenital heart defect in which the left side of the heart is severely underdeveloped. this causes a decrease in the amount of oxygenated blood pumped out of the heart, leading to inadequate oxygenation of the body’s tissues and organs. this condition is caused by a combination of genetic and environmental factors, including abnormal development of the heart during fetal development, genetic mutations, and exposure to certain environmental toxins. in some cases, hlhs may be associated with other congenital heart defects, such as aortic stenosis or atrial septal defects.

Clinical Pattern

More details coming soon

How does a doctor diagnose

  • Echocardiogram
  • Chest X-ray
  • Electrocardiogram (ECG)
  • Cardiac MRI
  • Cardiac catheterization
  • Blood tests
Additions:
  • Pulse oximetry
  • Ultrasound

Treatment and Medical Assistance

Main goal: Treating Hypoplastic left heart syndrome
  • Medication to help manage symptoms and reduce complications
  • Surgery to reconstruct the heart and improve blood flow
  • Heart transplantation
  • Regular monitoring of heart function
  • Lifestyle changes to reduce stress and improve overall health
  • Counseling to help cope with the emotional impact of the condition
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18 Days of Hospitalization Required
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Average Time for Outpatient Care Not Established

Hypoplastic left heart syndrome - Prevention

Hypoplastic left heart syndrome can be prevented by early detection and intervention during pregnancy. ultrasound and echocardiogram tests can be used to detect the condition before birth, allowing for timely corrective action and better outcomes for the baby.