(A81.0) Creutzfeldt-jakob disease

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34 594 in individuals diagnosis creutzfeldt-jakob disease confirmed
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23 959 deaths with diagnosis creutzfeldt-jakob disease
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69% mortality rate associated with the disease creutzfeldt-jakob disease

Diagnosis creutzfeldt-jakob disease is diagnosed Women are 13.30% more likely than Men

14 997

Men receive the diagnosis creutzfeldt-jakob disease

11 649 (77.7 %)

Died from this diagnosis.

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19 597

Women receive the diagnosis creutzfeldt-jakob disease

12 310 (62.8 %)

Died from this diagnosis.

Risk Group for the Disease creutzfeldt-jakob disease - Men aged 70-74 and Women aged 65-69

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In Men diagnosis is most often set at age 5-9, 20-24, 30-89
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Less common in men the disease occurs at Age 0-5, 10-19, 25-29, 90-95+Less common in women the disease occurs at Age 0-1, 5-14, 25-29, 90-95+
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In Women diagnosis is most often set at age 0-5, 15-24, 30-89

Disease Features creutzfeldt-jakob disease

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Absence or low individual and public risk
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Creutzfeldt-jakob disease - what does this mean

Creutzfeldt-jakob disease is caused by the abnormal folding of a protein called prion, which accumulates in the brain and leads to the death of nerve cells. this causes a rapid decline in mental and physical abilities, leading to death within a year of diagnosis.

What happens during the disease - creutzfeldt-jakob disease

Creutzfeldt-jakob disease (cjd) is a rare, progressive neurodegenerative disorder caused by the abnormal accumulation of a misfolded protein called prion in the brain. prion accumulation leads to the destruction of neurons, resulting in a variety of neurological symptoms, including dementia, ataxia, and myoclonus. the exact cause of cjd is unknown, however, it is believed that the misfolded prion protein is acquired through exposure to contaminated tissue or a genetic mutation.

Clinical Pattern

More details coming soon

How does a doctor diagnose

  • MRI scan
  • Spinal tap
  • Electroencephalogram (EEG)
  • Blood tests
  • Genetic testing
  • Brain biopsy
Additions:
  • Urine tests
  • Cerebrospinal fluid (CSF) analysis

Treatment and Medical Assistance

Main Goal: To slow down the progression of Creutzfeldt-Jakob Disease
  • Provide supportive care to manage symptoms
  • Prescribe medications to slow the progression of the disease
  • Refer patient to physical therapy for muscle strengthening and coordination
  • Refer patient to speech therapy to help with speech and swallowing difficulties
  • Refer patient to a nutritionist to help with dietary needs
  • Refer patient to a neurologist for monitoring of the disease
  • Provide patient and family with emotional and psychological support
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46 Days of Hospitalization Required
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Average Time for Outpatient Care Not Established

Creutzfeldt-jakob disease - Prevention

Creutzfeldt-jakob disease is a rare and fatal neurological disorder, and there is no known way to prevent it. however, there are some steps that can be taken to reduce the risk of infection, such as avoiding contact with the brain or spinal cord tissue of infected individuals, using sterile instruments during medical procedures, and avoiding the consumption of contaminated food products.