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(M34.1) Cr(e)st syndrome
More details coming soon
589 161 in individuals diagnosis cr(e)st syndrome confirmed
30 703 deaths with diagnosis cr(e)st syndrome
5% mortality rate associated with the disease cr(e)st syndrome
Diagnosis cr(e)st syndrome is diagnosed Women are 60.53% more likely than Men
116 268
Men receive the diagnosis cr(e)st syndrome
8 382 (7.2 %)Died from this diagnosis.
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472 893
Women receive the diagnosis cr(e)st syndrome
22 321 (4.7 %)Died from this diagnosis.
Risk Group for the Disease cr(e)st syndrome - Men aged 50-54 and Women aged 55-59
In Men diagnosis is most often set at age 5-89
Less common in men the disease occurs at Age 0-5, 90-95+Less common in women the disease occurs at Age 0-1, 90-95+
In Women diagnosis is most often set at age 0-89
Disease Features cr(e)st syndrome
Absence or low individual and public risk
Cr(e)st syndrome - what does this mean
Cr(e)st syndrome is an autoimmune disorder that occurs when a person's immune system mistakenly attacks their own connective tissue, leading to the formation of antibodies that cause inflammation, pain, and damage to the skin, joints, and other organs. symptoms of the disorder can include rashes, joint pain, and raynaud's phenomenon.
What happens during the disease - cr(e)st syndrome
Cr(e)st syndrome is a rare autoimmune disorder caused by the production of autoantibodies that attack the connective tissue of the skin, leading to the formation of fibrous bands in the skin and underlying tissues. this results in a variety of symptoms including skin thickening, scarring, and joint contractures. additionally, it can lead to systemic inflammatory and immune problems such as vasculitis and organ damage.
Clinical Pattern
More details coming soon
How does a doctor diagnose
- Physical exam
- Blood tests
- X-rays
- CT scans
- MRI scans
- Ultrasound exams
- Electrocardiogram (ECG)
- Echocardiogram (ECHO)
- Cardiac catheterization
Treatment and Medical Assistance
Main goal of the treatment: To reduce symptoms and improve quality of life for individuals with CR(E)ST syndrome
- Developing a treatment plan tailored to individual needs
- Managing medications to reduce inflammation
- Providing physical and occupational therapy
- Encouraging lifestyle changes, such as regular exercise and stress reduction
- Using assistive devices, such as braces and splints, to improve mobility
- Providing counseling and support for mental health issues
- Educating patients and families about the disease and its management
13 Days of Hospitalization Required
Average Time for Outpatient Care Not Established
Cr(e)st syndrome - Prevention
Cr(e)st syndrome prevention involves avoiding environmental triggers such as smoking, dust, and chemical exposure, as well as maintaining a healthy lifestyle with regular exercise and a balanced diet. additionally, it is important to get regular check-ups with a doctor to monitor for any early signs of the condition.