(M72.4) Pseudosarcomatous fibromatosis

More details coming soon

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1 557 126 in individuals diagnosis pseudosarcomatous fibromatosis confirmed
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19 817 deaths with diagnosis pseudosarcomatous fibromatosis
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1% mortality rate associated with the disease pseudosarcomatous fibromatosis

Diagnosis pseudosarcomatous fibromatosis is diagnosed Men are 62.18% more likely than Women

1 262 656

Men receive the diagnosis pseudosarcomatous fibromatosis

11 013 (0.9 %)

Died from this diagnosis.

100
95
90
85
80
75
70
65
60
55
50
45
40
35
30
25
20
15
10
5
0
294 470

Women receive the diagnosis pseudosarcomatous fibromatosis

8 804 (3.0 %)

Died from this diagnosis.

Risk Group for the Disease pseudosarcomatous fibromatosis - Men and Women aged 60-64

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In Men diagnosis is most often set at age 0-94
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Less common in men the disease occurs at Age 95+Less common in women the disease occurs at Age 0-5, 95+
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In Women diagnosis is most often set at age 5-94

Disease Features pseudosarcomatous fibromatosis

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Absence or low individual and public risk
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Pseudosarcomatous fibromatosis - what does this mean

Pseudosarcomatous fibromatosis is a rare, benign, non-hereditary soft tissue tumor of unknown origin that is characterized by a proliferation of spindle-shaped cells and collagen fibers. it is usually seen in adults in the extremities, particularly the upper arms and legs, and is often associated with a history of trauma or surgery in the affected area.

What happens during the disease - pseudosarcomatous fibromatosis

Pseudosarcomatous fibromatosis is a rare disorder of unknown etiology, characterized by the abnormal growth of fibrous tissue in the deep layers of the skin. it is thought to be caused by an underlying genetic mutation in the genes responsible for regulating cell growth and division, leading to the formation of fibrous tissue in the affected areas. the abnormal tissue growth may be further exacerbated by environmental factors, such as exposure to uv radiation, hormones, and certain medications.

Clinical Pattern

More details coming soon

How does a doctor diagnose

  • Physical examination
  • X-ray imaging
  • Magnetic resonance imaging (MRI)
  • Ultrasound
  • Biopsy
  • CT scan
  • Blood tests

Treatment and Medical Assistance

Main Goal: Treating Pseudosarcomatous Fibromatosis
  • Surgery to remove the tumor
  • Chemotherapy to reduce the size of the tumor
  • Radiation therapy to destroy cancer cells
  • Immunotherapy to stimulate the body's immune system to fight the disease
  • Targeted therapy to block the growth of cancer cells
  • Hormone therapy to reduce the growth of cancer cells
  • Pain management to reduce discomfort caused by the disease
  • Rehabilitation to help restore movement and strength
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7 Days of Hospitalization Required
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Average Time for Outpatient Care Not Established

Pseudosarcomatous fibromatosis - Prevention

Pseudosarcomatous fibromatosis can be prevented by avoiding contact with people who have the disease, practicing good hygiene, and avoiding exposure to environmental pollutants such as smoke and dust. additionally, it is important to maintain a healthy lifestyle, including regular exercise and a balanced diet. vaccines may also be available in some cases.