(D57.8) Other sickle-cell disorders

More details coming soon

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65 661 in individuals diagnosis other sickle-cell disorders confirmed
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2 472 deaths with diagnosis other sickle-cell disorders
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4% mortality rate associated with the disease other sickle-cell disorders

Diagnosis other sickle-cell disorders is diagnosed Men are 15.12% more likely than Women

37 794

Men receive the diagnosis other sickle-cell disorders

804 (2.1 %)

Died from this diagnosis.

100
95
90
85
80
75
70
65
60
55
50
45
40
35
30
25
20
15
10
5
0
27 867

Women receive the diagnosis other sickle-cell disorders

1 668 (6.0 %)

Died from this diagnosis.

Risk Group for the Disease other sickle-cell disorders - Men and Women aged 10-14

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In Men diagnosis is most often set at age 0-59, 65-89
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Less common in men the disease occurs at Age 60-64, 90-95+Less common in women the disease occurs at Age 50-54, 90-95+
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In Women diagnosis is most often set at age 0-49, 55-89

Disease Features other sickle-cell disorders

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Absence or low individual and public risk
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Other sickle-cell disorders - what does this mean

Other sickle-cell disorders occur when a person has one sickle cell gene and one normal gene. this causes the person to have hemoglobin s, which is a type of hemoglobin that can form long, rigid rods when exposed to low oxygen levels. this can cause red blood cells to become sickle shaped, leading to anemia, organ damage, and other complications.

What happens during the disease - other sickle-cell disorders

Other sickle-cell disorders are a group of inherited blood disorders that are caused by a mutation in the hemoglobin gene. this mutation causes an abnormal shape of the red blood cells, leading to a decrease in the oxygen-carrying capacity of the blood, an increased risk of clotting, and an increased risk of infection. this can lead to a range of symptoms, including anemia, fatigue, pain, organ damage, and increased risk of stroke.

Clinical Pattern

More details coming soon

How does a doctor diagnose

  • Complete Blood Count (CBC)
  • Hemoglobin Electrophoresis
  • Sickle Cell Solubility Test
  • Hemoglobin Fractionation
  • Genetic Testing
  • Bone Marrow Biopsy
  • Liver Function Tests
  • Kidney Function Tests
  • X-Rays

Treatment and Medical Assistance

Main Goal: Treating Other Sickle-Cell Disorders
  • Administering medications to reduce pain and inflammation
  • Encouraging adequate fluid intake to prevent dehydration
  • Providing oxygen therapy to improve oxygen levels in the blood
  • Prescribing antibiotics to prevent and treat infections
  • Administering blood transfusions to replace sickle cells with healthy ones
  • Encouraging regular exercise to increase circulation and reduce pain
  • Using hydroxyurea to reduce the production of sickle cells
  • Encouraging a healthy diet to maintain energy levels and reduce inflammation
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11 Days of Hospitalization Required
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Average Time for Outpatient Care Not Established

Other sickle-cell disorders - Prevention

The best way to prevent other sickle-cell disorders is to ensure that the patient receives regular medical care and is up to date on vaccinations. it is also important to maintain a healthy lifestyle, including eating a balanced diet, exercising regularly, and avoiding alcohol and tobacco use. additionally, it is important to get tested for sickle-cell traits and to be aware of any family history of the disorder.