(Q26.3) Partial anomalous pulmonary venous connection

More details coming soon

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48 491 in individuals diagnosis partial anomalous pulmonary venous connection confirmed
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3 041 deaths with diagnosis partial anomalous pulmonary venous connection
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6% mortality rate associated with the disease partial anomalous pulmonary venous connection

Diagnosis partial anomalous pulmonary venous connection is diagnosed Men are 14.31% more likely than Women

27 715

Men receive the diagnosis partial anomalous pulmonary venous connection

1 831 (6.6 %)

Died from this diagnosis.

100
95
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75
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65
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55
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15
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20 776

Women receive the diagnosis partial anomalous pulmonary venous connection

1 210 (5.8 %)

Died from this diagnosis.

Risk Group for the Disease partial anomalous pulmonary venous connection - Men and Women aged 0

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In Men diagnosis is most often set at age 0-29, 35-64, 75-79
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Less common in men the disease occurs at Age 30-34, 65-74, 80-95+Less common in women the disease occurs at Age 70-79, 85-95+
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In Women diagnosis is most often set at age 0-69, 80-84

Disease Features partial anomalous pulmonary venous connection

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Absence or low individual and public risk
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Partial anomalous pulmonary venous connection - what does this mean

Partial anomalous pulmonary venous connection is a congenital heart defect that occurs when one or more of the pulmonary veins that carry oxygen-rich blood from the lungs to the heart is abnormally connected to an artery or another vein instead of the left atrium. this defect can cause serious health problems and lead to heart failure if not treated.

What happens during the disease - partial anomalous pulmonary venous connection

Partial anomalous pulmonary venous connection is a congenital condition in which one or more of the pulmonary veins do not connect to the left atrium, but instead connect to another area of the heart. this can lead to a right-to-left shunt, where oxygenated blood from the lungs is diverted away from the left atrium and mixes with deoxygenated blood in the right atrium. this can lead to an increase in pulmonary artery pressure, resulting in pulmonary hypertension and right-sided heart failure.

Clinical Pattern

More details coming soon

How does a doctor diagnose

  • Echocardiography
  • Cardiac catheterization
  • Cardiac MRI
  • Chest X-ray
  • Pulmonary angiography
  • Electrocardiogram (ECG)

Treatment and Medical Assistance

Main Goal: To treat Partial anomalous pulmonary venous connection
  • Diagnosis through physical examination and medical imaging
  • Open heart surgery to repair the pulmonary veins
  • Closing the abnormal connection with stitches
  • Relieving the pressure on the right side of the heart
  • Replacing the pulmonary veins with a graft
  • Medications to reduce the risk of blood clots
  • Follow-up care to monitor the heart's functioning
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21 Days of Hospitalization Required
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Average Time for Outpatient Care Not Established

Partial anomalous pulmonary venous connection - Prevention

Partial anomalous pulmonary venous connection is best prevented by early detection and treatment of any underlying congenital heart defects. as this condition is often associated with other heart defects, regular prenatal screenings and monitoring of infants and young children are recommended to identify any potential issues and treat them promptly.