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(Q22.6) Hypoplastic right heart syndrome
More details coming soon
258 814 in individuals diagnosis hypoplastic right heart syndrome confirmed
5 601 deaths with diagnosis hypoplastic right heart syndrome
2% mortality rate associated with the disease hypoplastic right heart syndrome
Diagnosis hypoplastic right heart syndrome is diagnosed Men are 2.44% more likely than Women
132 569
Men receive the diagnosis hypoplastic right heart syndrome
3 043 (2.3 %)Died from this diagnosis.
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126 245
Women receive the diagnosis hypoplastic right heart syndrome
2 558 (2.0 %)Died from this diagnosis.
Risk Group for the Disease hypoplastic right heart syndrome - Men and Women aged 0
In Men diagnosis is most often set at age 0-79
Less common in men the disease occurs at Age 80-95+Less common in women the disease occurs at Age 80-95+
In Women diagnosis is most often set at age 0-79
Disease Features hypoplastic right heart syndrome
Absence or low individual and public risk
Hypoplastic right heart syndrome - what does this mean
Hypoplastic right heart syndrome is a congenital heart defect in which the right side of the heart is underdeveloped, resulting in inadequate blood flow to the lungs. this can result in decreased oxygen levels in the blood, leading to a wide range of symptoms, including difficulty breathing, fatigue, and poor growth.
What happens during the disease - hypoplastic right heart syndrome
Hypoplastic right heart syndrome (hrhs) is a congenital heart defect that occurs when the right side of the heart does not develop properly. this results in the right ventricle and right atrium being underdeveloped and unable to effectively pump blood to the lungs. this can cause a decrease in oxygen levels in the blood, leading to hypoxemia, and a buildup of blood in the lungs, leading to pulmonary hypertension. the decreased blood flow can also lead to a decrease in blood pressure, resulting in decreased perfusion to the body.
Clinical Pattern
More details coming soon
How does a doctor diagnose
- Echocardiogram
- Chest X-ray
- Cardiac MRI
- Electrocardiogram (ECG)
- Cardiac catheterization
- Cardiac CT scan
- Blood tests
Treatment and Medical Assistance
Main Goal: To improve the symptoms of Hypoplastic right heart syndrome
- Medication to reduce pulmonary artery pressure
- Surgery to create a shunt between the right ventricle and the pulmonary artery
- Surgery to create a shunt between the left atrium and the pulmonary artery
- Surgery to enlarge the right ventricle
- Surgery to create an artificial valve between the right ventricle and the pulmonary artery
- Surgery to create an artificial valve between the left atrium and the pulmonary artery
- Surgery to replace the right ventricle with a mechanical device
- Surgery to replace the pulmonary artery with a mechanical device
- Surgery to bypass the right ventricle and the pulmonary artery
- Surgery to bypass the left atrium and the pulmonary artery
- Surgery to implant a pacemaker to regulate heart rate
- Surgery to implant a defibrillator to regulate heart rhythm
- Medication to reduce swelling in the lungs
- Medication to reduce inflammation in the lungs
- Medication to reduce fluid buildup in the lungs
15 Days of Hospitalization Required
Average Time for Outpatient Care Not Established
Hypoplastic right heart syndrome - Prevention
Hypoplastic right heart syndrome is a congenital heart defect that can be prevented by early and regular prenatal care. this includes regular ultrasounds and monitoring of the mother's health and nutrition, as well as taking folic acid supplements to reduce the risk of neural tube defects. additionally, avoiding alcohol, tobacco, and illegal drugs during pregnancy can help to reduce the risk of this heart defect.